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KMID : 0371620080230020191
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Journal of Wonkwang Medical Science
2008 Volume.23 No. 2 p.191 ~ p.194
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A case of Rotor syndrome with typical DISIDA scan finding
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Hwang Eui-Tae
Yeom Dong-Han
Kwon Ji-Hye
Im Chong-Ju
Choi Chang-Soo
Kim Tae-Hyeon
Kim Haak-Cheol
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Abstract
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Chronic nonhemolytic conjugated hyperbilirubinemia characterizes both Rotor and Dubin-Johnson syndromes. Rotor syndrome is a rare, benign familial disorder and needs to be differentiated from Dubin-Johnson syndrome. Cholescintigraphy is a simple and informative procedure for the diagnosis, which can differentiate Rotor syndrome from Dubin-Johnson syndrome. A 26-year-old man was admitted due to asymptomatic persistent jaundice. Physical examination revealed icteric sclera without hepatosplenomegaly. Laboratory findings showed increased serum bilirubin with direct bilirubinemia. Markedly decreased hepatic uptake and poor visualization of the gallbladder and biliary tract were shown in ^(99m)Tc-DISIDA scan. Histology of the liver showed no diagnostic abnormality without pigmentation. But, we report a case of Rotor syndrome that showed characteristic cholescintigraphic findings with normal urinary total coproporphyrin excretion.
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KEYWORD
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Hyperbilirubinemia, Hereditary, Jaundice, Technetium Tc 99m Disofenin
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